Esophageal Atresia Associated with Congenital Duodenal Obstruction: Turkish Esophageal Atresia Registry (TEAR) Evaluation
dc.authorid | firinci, binali/0000-0002-0852-2458 | |
dc.authorid | Ulukaya Durakbasa, Cigdem/0000-0002-6474-3407 | |
dc.authorid | Caliskan, Dogus/0000-0001-7168-2123 | |
dc.authorid | OZTAN, Mustafa Onur/0000-0003-3696-4090 | |
dc.authorid | Ozcan, Rahsan/0000-0002-8873-2841 | |
dc.authorid | Soyer, Tutku/0000-0003-1505-6042 | |
dc.authorid | Ozcakir, Esra/0000-0002-0773-7430 | |
dc.contributor.author | Durakbasa, Cigdem Ulukaya | |
dc.contributor.author | Soyer, Tutku | |
dc.contributor.author | Ilhan, Hueseyin | |
dc.contributor.author | Oztan, Mustafa Onur | |
dc.contributor.author | Uzunlu, Osman | |
dc.contributor.author | Firinci, Binali | |
dc.contributor.author | Ozcan, Rahsan | |
dc.date.accessioned | 2024-10-29T17:58:33Z | |
dc.date.available | 2024-10-29T17:58:33Z | |
dc.date.issued | 2024 | |
dc.department | Tekirdağ Namık Kemal Üniversitesi | |
dc.description.abstract | Introduction Coexistent congenital duodenal obstruction and esophageal atresia (EA) is known to have significant morbidity and mortality. Management strategies are not well-defined for this association. The data fromthe Turkish EA registry is evaluated. Materials and Methods A database search was done for the years 2015 to 2022. Results Among 857 EA patients, 31 (3.6%) had congenital duodenal obstruction. The mean birth weight was 2,104 (+/- 457) g with 6 babies weighing less than 1,500 g. Twenty-six (84%) had type C EA. The duodenal obstruction was complete in 15 patients and partial in 16. Other anomalies were detected in 27 (87%) patients. VACTERL-H was present in 15 (48%), anorectal malformation in 10 (32%), amajor cardiacmalformation in 6 (19%), and trisomy-21 in 3 (10%). Duodenal obstruction diagnosiswas delayed in 10 ( 32%) babies for a median of 7.5 (1-109) days. Diagnosis for esophageal pathologies was delayed in 2. Among 19 babies with a simultaneous diagnosis, 1 died without surgery, 6 underwent triple repair for tracheoesophageal fistula (TEF), EA, and duodenal obstruction, and 3 for TEF and duodenal obstruction in the same session. A staged repair was planned in the remaining 9 patients. In total, 15 ( 48%) patients received a gastrostomy, the indication was long-gap EA in 8. Twenty-five (77%) patients survived. The cause of mortality was sepsis (n = 3) and major cardiac malformations (n = 3). Conclusion Congenital duodenal obstruction associated with EA is a complex problem. Delayed diagnosis is common. Management strategies regarding singlestage repairs or gastrostomy insertions vary notably depending on the patient characteristics and institutional preferences. | |
dc.identifier.doi | 10.1055/a-2123-5026 | |
dc.identifier.endpage | 49 | |
dc.identifier.issn | 0939-7248 | |
dc.identifier.issn | 1439-359X | |
dc.identifier.issue | 1 | en_US |
dc.identifier.pmid | 37406676 | |
dc.identifier.scopus | 2-s2.0-85165284256 | |
dc.identifier.scopusquality | Q2 | |
dc.identifier.startpage | 44 | |
dc.identifier.uri | https://doi.org/10.1055/a-2123-5026 | |
dc.identifier.uri | https://hdl.handle.net/20.500.11776/14387 | |
dc.identifier.volume | 34 | |
dc.identifier.wos | WOS:001045010100002 | |
dc.identifier.wosquality | Q2 | |
dc.indekslendigikaynak | Web of Science | |
dc.indekslendigikaynak | Scopus | |
dc.indekslendigikaynak | PubMed | |
dc.language.iso | en | |
dc.publisher | Georg Thieme Verlag Kg | |
dc.relation.ispartof | European Journal of Pediatric Surgery | |
dc.relation.publicationcategory | Makale - Uluslararası Hakemli Dergi - Kurum Öğretim Elemanı | en_US |
dc.rights | info:eu-repo/semantics/closedAccess | |
dc.subject | esophageal atresia | |
dc.subject | duodenal atresia | |
dc.subject | management | |
dc.subject | surgery | |
dc.subject | outcome | |
dc.title | Esophageal Atresia Associated with Congenital Duodenal Obstruction: Turkish Esophageal Atresia Registry (TEAR) Evaluation | |
dc.type | Article |