Esophageal Atresia Associated with Congenital Duodenal Obstruction: Turkish Esophageal Atresia Registry (TEAR) Evaluation

dc.authoridfirinci, binali/0000-0002-0852-2458
dc.authoridUlukaya Durakbasa, Cigdem/0000-0002-6474-3407
dc.authoridCaliskan, Dogus/0000-0001-7168-2123
dc.authoridOZTAN, Mustafa Onur/0000-0003-3696-4090
dc.authoridOzcan, Rahsan/0000-0002-8873-2841
dc.authoridSoyer, Tutku/0000-0003-1505-6042
dc.authoridOzcakir, Esra/0000-0002-0773-7430
dc.contributor.authorDurakbasa, Cigdem Ulukaya
dc.contributor.authorSoyer, Tutku
dc.contributor.authorIlhan, Hueseyin
dc.contributor.authorOztan, Mustafa Onur
dc.contributor.authorUzunlu, Osman
dc.contributor.authorFirinci, Binali
dc.contributor.authorOzcan, Rahsan
dc.date.accessioned2024-10-29T17:58:33Z
dc.date.available2024-10-29T17:58:33Z
dc.date.issued2024
dc.departmentTekirdağ Namık Kemal Üniversitesi
dc.description.abstractIntroduction Coexistent congenital duodenal obstruction and esophageal atresia (EA) is known to have significant morbidity and mortality. Management strategies are not well-defined for this association. The data fromthe Turkish EA registry is evaluated. Materials and Methods A database search was done for the years 2015 to 2022. Results Among 857 EA patients, 31 (3.6%) had congenital duodenal obstruction. The mean birth weight was 2,104 (+/- 457) g with 6 babies weighing less than 1,500 g. Twenty-six (84%) had type C EA. The duodenal obstruction was complete in 15 patients and partial in 16. Other anomalies were detected in 27 (87%) patients. VACTERL-H was present in 15 (48%), anorectal malformation in 10 (32%), amajor cardiacmalformation in 6 (19%), and trisomy-21 in 3 (10%). Duodenal obstruction diagnosiswas delayed in 10 ( 32%) babies for a median of 7.5 (1-109) days. Diagnosis for esophageal pathologies was delayed in 2. Among 19 babies with a simultaneous diagnosis, 1 died without surgery, 6 underwent triple repair for tracheoesophageal fistula (TEF), EA, and duodenal obstruction, and 3 for TEF and duodenal obstruction in the same session. A staged repair was planned in the remaining 9 patients. In total, 15 ( 48%) patients received a gastrostomy, the indication was long-gap EA in 8. Twenty-five (77%) patients survived. The cause of mortality was sepsis (n = 3) and major cardiac malformations (n = 3). Conclusion Congenital duodenal obstruction associated with EA is a complex problem. Delayed diagnosis is common. Management strategies regarding singlestage repairs or gastrostomy insertions vary notably depending on the patient characteristics and institutional preferences.
dc.identifier.doi10.1055/a-2123-5026
dc.identifier.endpage49
dc.identifier.issn0939-7248
dc.identifier.issn1439-359X
dc.identifier.issue1en_US
dc.identifier.pmid37406676
dc.identifier.scopus2-s2.0-85165284256
dc.identifier.scopusqualityQ2
dc.identifier.startpage44
dc.identifier.urihttps://doi.org/10.1055/a-2123-5026
dc.identifier.urihttps://hdl.handle.net/20.500.11776/14387
dc.identifier.volume34
dc.identifier.wosWOS:001045010100002
dc.identifier.wosqualityQ2
dc.indekslendigikaynakWeb of Science
dc.indekslendigikaynakScopus
dc.indekslendigikaynakPubMed
dc.language.isoen
dc.publisherGeorg Thieme Verlag Kg
dc.relation.ispartofEuropean Journal of Pediatric Surgery
dc.relation.publicationcategoryMakale - Uluslararası Hakemli Dergi - Kurum Öğretim Elemanıen_US
dc.rightsinfo:eu-repo/semantics/closedAccess
dc.subjectesophageal atresia
dc.subjectduodenal atresia
dc.subjectmanagement
dc.subjectsurgery
dc.subjectoutcome
dc.titleEsophageal Atresia Associated with Congenital Duodenal Obstruction: Turkish Esophageal Atresia Registry (TEAR) Evaluation
dc.typeArticle

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